McCune-Albright syndrome 환자의 치과적 특성
DENTAL CHARACTERISTICS OF A PATIENT WITH MCCUNE-ALBRIGHT SYNDROME
임재영, 송제선, 이고은, 이제호,
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임재영 ( Lim Jae-Young ) - 연세대학교 치과대학 소아치과학교실
송제선 ( Song Je-Seon ) - 연세대학교 치과대학 소아치과학교실
이고은 ( Lee Ko-Eun ) - 연세대학교 치과대학 소아치과학교실
이제호 ( Lee Jae-Ho ) - 연세대학교 치과대학 소아치과학교실
Abstract
McCune-Albright syndrome (MAS) is a rare disease characterized by fibrous dysplasia (FD), Cafe-au-lait spots, and endocrine disorder. A 4-year-old girl with MAS visited the clinic with a chief complaint of facial asymmetry and bruxism without any pain. Facial asymmetry and many dental problems such as midline deviation, “ground glass appearance” on the entire jaw, thinned cortical bone, loss of lamina dura and ectopic germs were found. Because of severely displaced tooth germs and FD affected jaw, there is a high possibility of malocclusion during mixed/permanent dentition. It is necessary to observe the eruption pattern periodically. If there are clinical symptoms like an abnormal eruption pattern, facial asymmetry or high caries susceptibility, appropriate interventions of dentist are required.
키워드
McCune-Albright syndrome; Fibrous dysplasia; Facial asymmetry
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